Carbohydrate Metabolism — Flashcards

Von Gierke disease is characterized by very increased levels of _____ in the liver and kidneys, with subsequent hepatomegaly and renomegaly

Fructose-1,6-bisphosphatase is regulated via negative feedback by _____ and AMP

When insulin acts on liver tissue, it causes _____ glycogenesis and decreased glycogenolysis

What symptoms does essential fructosuria typically present with?_____

_____ disease occurs due to a defect in the enzyme muscle phosphofructokinase.

_____ is ultimately converted to ribulose-5-phosphate via the enzyme glucose-6-phosphate dehydrogenase

_____ results in the formation of α-1,6 bonds between glucose molecules

Glucose-6-phosphate is converted to _____ via the enzyme glucose-6-phosphatase

_____ liberates glucose-1-phosphate residues off branched glycogen until 4 glucose units remain on a branch

Large amounts of _____ are given for treatment of abetalipoproteinemia so that excess will be converted to short-chain fatty acids in the colon.