Carbohydrate Metabolism — Flashcards

_____ disease is also known as glycogen storage disease type III

Glycogen stores typically are depleted after _____ - 18 hours

Cori disease is characterized by _____ gluconeogenesis and impaired glycogenolysis (impaired or functional)

_____ disease is caused by a deficiency of the enzyme debranching enzyme (-1,6-glucosidase)

Treatment of Von Gierke disease includes avoidance of _____, galactose, sucrose, and lactose

Von Gierke disease is characterized by _____ gluconeogenesis and impaired glycogenolysis (impaired or functional)

Von Gierke disease is associated with increased blood _____ate, triglycerides, and uric acid

Von Gierke disease is characterized by very increased levels of _____ in the liver and kidneys, with subsequent hepatomegaly and renomegaly

What symptoms does essential fructosuria typically present with?_____

Fructose-1,6-bisphosphatase is regulated via negative feedback by _____ and AMP