Amino Acid Metabolism — Flashcards

_____ (from tyrosine) may be converted to maleylacetoacetate via the enzyme homogentisate oxidase

_____ and valine are eventually broken down into propionyl-CoA via the enzyme branched-chain -ketoacid dehydrogenase

Hartnup disease is treated with a high-_____ diet and nicotinic acid (niacin)

Vitamins required for the conversion of serine to glycine are _____ and folic acid

_____ may be converted to epinephrine via the enzyme phenylethanolamine-N-methyltransferase (with SAM as a cofactor) and stimulated by cortisol

Type _____ maple syrup urine disease (MSUD) results from the mutation in the genes encoding dihydrolipoyl transacylase.

_____ may be converted to cystathionine via the enzyme cystathionine synthase (with B6 as a cofactor)

_____ disease is due to a deficiency of neutral amino acid transporters (especially tryptophan) in the proximal renal tubular cells and enterocytes

Phenylketones include _____, phenyllactate, and phenylpyruvate

_____ is converted to dihydroxyphenylalanine (DOPA) via the enzyme tyrosine hydroxylase (with tetrahydrobiopterin as a cofactor)