Amino Acid Metabolism — Flashcards

Carbamoyl phosphate synthetase I deficiency presents with _____ NH4+ and hyper-ammonemia

Vitamins required for the conversion of serine to glycine are _____ and folic acid

_____ is eventually broken down into acetyl-CoA via the enzyme branched-chain α-ketoacid dehydrogenase

Hartnup disease is treated with a high-_____ diet and nicotinic acid (niacin)

In the liver, alanine transfers its NH3 group to _____, forming glutamate and pyruvate

_____ may be converted to melanin via the enzyme tyrosinase

Arginine may be broken down into _____ and urea via the enzyme arginase

_____ may be converted to epinephrine via the enzyme phenylethanolamine-N-methyltransferase (with SAM as a cofactor) and stimulated by cortisol

_____ may be converted to dopamine via the enzyme DOPA decarboxylase (with vitamin B6 as a cofactor)

The urea cycle begins with _____, CO2, and 2 ATP