FMGE 2023 - Pediatrics Practice Questions

Q: Which of the following is not a correct match for ABCD according to pediatric advanced life support?

Dehydration. ***Dehydration*** - In the mnemonic **ABCD** used in **Pediatric Advanced Life Support (PALS)** and basic life support (BLS), D stands for **Disability** (neurological status/deficit), not Dehydration. - Assessing **Disability** involves evaluating the infant's or child's neurological status using tools like the **AVPU scale** or **Glasgow Coma Scale (GCS)**. *Airway* - A stands correctly for **Airway** in the **ABCD** approach, focusing on ensuring a patent passage for breathing. - This step involves opening the airway using maneuvers like the **head tilt/chin lift** (for trauma absence) or **jaw thrust** (for suspected trauma). *Breathing* - B stands correctly for **Breathing**, which assesses the presence and adequacy of respiratory effort. - Management includes providing rescue breaths, using devices like a **bag-mask device**, and determining the need for **intubation**. *Circulation* - C stands correctly for **Circulation**, which evaluates heart rate, pulse strength, capillary refill time, and skin color. - Interventions include initiating **chest compressions** if a pulse is absent or too slow/weak, and managing **shock** (e.g., fluid resuscitation/medications).

Q: A child has elevated liver enzyme levels. A ring-like structure is noted on ocular examination. Which of the following is the cause for this?

Copper. ***Copper***- The combination of elevated **liver enzymes** (hepatitis/cirrhosis) and the characteristic **Kayser-Fleischer (KF) rings** visible on ocular examination is pathognomonic for **Wilson's disease**.- **Wilson's disease** is an inherited disorder involving defective biliary excretion of **copper**, causing its toxic accumulation in tissues, notably the liver, brain, and cornea.*Zinc*- Zinc is an essential trace element, but its deficiency presents primarily with **acrodermatitis enteropathica**, not hepatic failure and KF rings.- Zinc supplementation is sometimes used as a treatment for Wilson's disease because it inhibits the absorption of **copper** in the gut.*Selenium*- Deficiency of **Selenium** is associated with **Keshan disease** (cardiomyopathy) and impaired antioxidant protection, rather than liver disease with corneal rings.- High levels of selenium, though rare, can lead to hair loss and nail changes (**selenosis**).*Iron*- Excessive accumulation of **Iron** causes **hemochromatosis**, which leads to hepatomegaly, cirrhosis, and **bronze diabetes**.- Iron overload does not result in the formation of **Kayser-Fleischer rings**; these rings are exclusively caused by **copper** deposition in the Descemet membrane.

Q: A neonate was brought with a history of frothiness from the mouth and respiratory distress. An X-ray of the neonate is given below. What is the diagnosis?

Esophageal atresia with tracheo-esophageal fistula. ***Esophageal atresia with tracheo-esophageal fistula*** - The clinical presentation of a neonate with excessive **frothiness from the mouth**, choking, and **respiratory distress** is highly suggestive of this diagnosis. - The X-ray confirms the diagnosis by showing a **coiled orogastric tube** (indicated by the arrow) in the blind-ending upper esophageal pouch. The presence of **gas in the stomach** indicates a communication between the trachea and the distal esophagus (a distal fistula). *Transient tachypnea of newborn* - This is a benign condition caused by delayed clearance of fetal lung fluid, presenting with rapid breathing shortly after birth, usually in term infants delivered by C-section. - The chest X-ray typically shows **perihilar streaking**, **fluid in the fissures**, and mild hyperinflation, not a coiled feeding tube. *Congenital diaphragmatic hernia* - This condition involves the herniation of abdominal contents into the chest, causing severe respiratory distress and a **scaphoid abdomen**. - The chest X-ray would show **bowel loops within the thoracic cavity** and displacement of the mediastinum, which are not seen in this image. *Respiratory distress syndrome* - Primarily seen in premature infants, this is caused by a deficiency of **pulmonary surfactant**. - The characteristic X-ray findings include low lung volumes, a diffuse **ground-glass appearance**, and **air bronchograms**.

Q: Which of the following are true about nephroblastoma except:

Treatment is chemotherapy followed by surgery. ***Correct Answer: Treatment is chemotherapy followed by surgery*** This is the **INCORRECT** statement (which makes it the correct answer for this EXCEPT question): - In **COG (Children's Oncology Group) protocol** used in India and US: **Primary treatment is upfront nephrectomy** (surgery first) followed by chemotherapy - SIOP protocol uses preoperative chemotherapy, but this is NOT the standard approach in India/FMGE context - **Surgery-first approach** allows for accurate staging and immediate tumor removal *Incorrect: Most common intra abdominal malignancy in children* - This is **TRUE** - Nephroblastoma (Wilms tumor) is indeed the most common intra-abdominal malignancy in children (peak age 3-4 years) *Incorrect: Early lung mets* - This is **TRUE** - Wilms tumor has propensity for **early hematogenous spread to lungs** - Lungs are the most common site of metastasis - Chest X-ray/CT is mandatory for staging *Incorrect: Hematogenous spread* - This is **TRUE** - Wilms tumor spreads via **hematogenous route** to lungs (most common), liver, and other sites - Unlike neuroblastoma which can spread lymphatically

Question 1

Which of the following is not a correct match for ABCD according to pediatric advanced life support?

Accepted Answer

Dehydration

Answer

Circulation

Answer

Airway

Answer

Breathing

Question 2

A child has elevated liver enzyme levels. A ring-like structure is noted on ocular examination. Which of the following is the cause for this?

Accepted Answer

Copper

Answer

Zinc

Answer

Selenium

Answer

Iron

Question 3

A neonate was brought with a history of frothiness from the mouth and respiratory distress. An X-ray of the neonate is given below. What is the diagnosis?

Accepted Answer

Esophageal atresia with tracheo-esophageal fistula

Answer

Transient tachypnea of newborn

Answer

Respiratory distress syndrome

Answer

Congenital diaphragmatic hernia

Question 4

Which of the following are true about nephroblastoma except:

Accepted Answer

Treatment is chemotherapy followed by surgery

Answer

Most common intra abdominal malignancy in children

Answer

Early lung mets

Answer

Hematogenous spread

FMGE 2023 — Pediatrics