Congenital Liver Diseases — MCQs

4 day old breastfed neonate, otherwise well, term neonate presented with jaundice, on testing the bilirubin level was found to be 18 mg/dl. Which of the following is the best step of management?

Absence of the intrahepatic bile ducts leads to which syndrome?

A patient with biliary atresia is more prone to the deficiency of:

What is the next step in managing a 3-day-old neonate with a bilirubin level of 18 mg/dL?

An 11-year-old boy was brought to the outpatient clinic with intention tremor and poor scholastic performance. His sister has similar complaints. On examination, hepatomegaly is seen. The eye finding is shown in the image. What is the probable diagnosis?

Which of the following statements about Gilbert syndrome is false?

Which of the following is a histopathological feature of extrahepatic biliary atresia?

Mallory bodies are typically seen in all of the following conditions except:

Micronodular cirrhosis is seen in all except:

Dubin-Johnson syndrome characteristically makes the liver darkly pigmented.