Urea Cycle — MCQs

Ammonia in brain is trapped by

Hyperammonaemia inhibits the TCA cycle by depleting which of the following?

Ammonia formed in the brain is converted into

Ammonia is detoxified in brain to :

Which will activate carbamoyl phosphate synthase I?

Most common enzyme deficiency in the urea cycle is:

Which of the following enzymes is not involved in the urea cycle?

Which enzyme deficiency is responsible for Hyperammonemia type-1?

Transamination of Alanine results in formation of ?

A 2-month-old infant presents with vomiting, lethargy, and metabolic acidosis. Blood tests reveal elevated levels of ammonia. What is the most likely diagnosis?