Hirschsprung disease management — Flashcards

Flashcard 1: Short bowel syndrome is most commonly seen in patients who have had _____

Answer: small intestine resection

Flashcard 2: _____ is a congenital hypertrophy of the pyloric smooth muscle

Answer: Pyloric stenosis

Flashcard 3: Treatment of Hirschsprung disease involves _____ of the involved bowel

Answer: resection

Flashcard 4: Peritonsillar Abscess is managed with _____

Answer: Drainage and IV antibiotics

Extra:  https://onlinemeded.org/spa/pediatrics/upper-airway/acquire?ref=anki 

Flashcard 5: Herniated contents may be at risk for _____, which is the inability to reduce contents back into the abdomen/pelvis

Answer: incarceration

Flashcard 6: What is the treatment for congenital hydrocephalus?_____

Answer: Ventriculoperitoneal shunt

Flashcard 7: What is the most common cause of small bowel obstruction? _____

Answer: Adhesion

Flashcard 8: What is the most common embryological origin of a congenital pharyngo-cutaneous fistula?

Answer: Persistence of the 2nd branchial cleft and pouch.

Extra: Congenital pharyngo-cutaneous fistulas (branchial fistulas) most commonly arise from the second branchial arch. The fistula typically tracks from the tonsillar fossa (pouch origin), between the internal and external carotid arteries, and opens onto the skin at the lower third of the neck anterior to the sternocleidomastoid muscle. 3rd/4th arch remnants are much rarer and typically involve the pyriform sinus.

Flashcard 9: Definition and key feature of Gastroschisis:

Answer: Extrusion of abdominal contents through abdominal folds, not covered by peritoneum.

Extra: Gastroschisis occurs due to a failure of involution of the right umbilical vein or a vascular accident involving the omphalomesenteric artery. It is typically found to the right of the umbilical cord insertion. Unlike omphalocele, it is NOT covered by a sac (peritoneum).

Flashcard 10: What are the 5 types of tracheoesophageal anomalies (Gross classification)?

Answer: 1. Pure Esophageal Atresia (EA) 2. EA with distal Tracheoesophageal Fistula (TEF) (Most common) 3. Pure TEF (H-type / no atresia) 4. EA with proximal TEF 5. EA with double TEF (both proximal and distal)

Extra: These correspond to the Gross classification of EA/TEF: - Type A: Pure EA - Type B: EA with proximal TEF - Type C: EA with distal TEF (~85% of cases) - Type D: EA with both proximal and distal TEF - Type E: H-type (Pure TEF without atresia)