Fatty acid oxidation (beta-oxidation) — Flashcards

_____ deficiency is an inherited defect in the transport of long chain fatty acids into the mitochondria

_____ CoA is the only fatty acid carbon that may be used to make glucose (via gluconeogenesis)

_____ deficiency is characterized by an inability to break down medium-sized fatty acids

What is the rate-limiting enzyme of fatty acid beta-oxidation?

Primary carnitine deficiency is characterized by muscle weakness and hypotonia, which is provoked by prolonged _____ (especially if fasting)

lipoamide

Where does fatty acid oxidation take place?

Where does fatty acid synthesis take place?

Where does steroid synthesis take place?

Where does cholesterol synthesis take place?