Hemoglobinopathies — Flashcards

Hb _____ levels are increased in juvenile chronic myeloid leukemia (JMML)

Patients with beta-thalassemia major are at risk of _____ with parvovirus B19 infection of erythroid precursors

Anaemia in a 2-5 year old child is defined as a hemoglobin level of

Beta-thalassemia _____ is characterized by expansion of hematopoiesis into facial bones, leading to "chipmunk facies"

Patients with Down syndrome, who develop transient myeloproliferative disorder require close follow-up, because 20 30% will develop _____ leukemia by 3 years of life

Acute chest syndrome is defined as a new _____ on CXR along with fever, respiratory distress, hypoxia, cough, or chest pain in a pt. with sickle cell disease

On complete blood count, patients with Systemic Juvenile Idiopathic Arthritis will frequently present with: - _____ RBCs - increased WBCs - increased Platelets

_____ syndrome is a syndrome of thrombocytopenia and consumptive coagulopathy in a patient of hemangioma

Kids with sickle cell disease should undergo _____ starting at age of 2 yrs to reduce the incidence of overt stroke