Homocystinuria and Methionine Metabolism — Flashcards

Homocystinuria and Methionine Metabolism — Flashcards

Homocystinuria and Methionine Metabolism — Flashcards
#1

The treatment for propionic acidemia is a low _____ diet that does not include valine, methionine, isoleucine, or threonine

#2

In addition to enzyme deficiencies, homocystinuria may be caused by decreased affinity of _____ for pyridoxal phosphate (B6, active form)

#3

_____ may be converted to cystathionine via the enzyme cystathionine synthase (with B6 as a cofactor)

#4

pulses are deficient in _____ amino acids

#5

cereals are deficient in _____ amino acids

#6

taurine amino acid is essential for _____

#7

breast milk is rich in _____ essential amino acids

#8

maize is deficient in _____ amino acids

#9

_____ amino acid is essential for premature children

#10

Carbamoyl phosphate synthetase I deficiency presents with _____ NH4+ and hyper-ammonemia

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Homocystinuria and Methionine Metabolism Flashcards | Amino Acid Metabolism Study Cards - OnCourse