Urea cycle — Flashcards

Carbamoyl phosphate synthetase I deficiency presents with _____ glutamine

Which tissue/organ uses NH3 as its major transport form of NH3? _____

Carbamoyl phosphate synthetase I is regulated via positive feedback by _____

In the intestine, NH3 may be produced via the breakdown of the amino acid _____

Most disorders of the urea cycle require _____ as an essential amino acid, particularly during episodes of hyperammonemia

What class of enzymes is used in the transfer of NH3 groups during nitrogen metabolism?_____

Urease positive organisms hydrolyze urea to _____, causing urine alkalinization

Part of the treatment for hyperammonemia is limiting _____ in the diet

Hyperammonemia results in excess NH3, which depletes _____, leading to inhibition of the TCA cycle

When an amino acid is metabolized, it is broken down into a carbon skeleton and _____ (highly toxic)