Urea cycle — Flashcards

Does carbamoyl phosphate synthetase I deficiency present with orotic aciduria? _____

Arginine may be broken down into _____ and urea via the enzyme arginase

Does the urea cycle occur in the cytoplasm or mitochondria? _____

Carbamoyl phosphate synthetase I deficiency presents with _____ NH4+ and _____-ammonemia

Ornithine transcarbamylase (OTC) deficiency presents with _____ serum glutamine

When an amino acid is metabolized, it is broken down into a carbon skeleton and _____ (highly toxic)

Carbamoyl phosphate synthetase I deficiency presents with _____ BUN

Does ornithine transcarbamylase deficiency present with orotic aciduria? _____

Ornithine transcarbamylase (OTC) deficiency presents with _____ NH4+ and _____-ammonemia

Disorders of the urea cycle interfere with the body's ability to eliminate _____