Amino Acid Metabolism — Flashcards

_____ in eukaryotes is also known as 21st amino acid

Urine FeCl3 test done for PKU detects the presence of _____

Plasma levels of _____ are elevated in gyrate atrophy of retina and choroid.

How does hyperammonenemia deplete alpha-ketoglutarate?_____

The amount of _____ excreted in the urine is directly proportional to muscle mass

What kind of odour is seen in Hawkinsinuria?_____

HHH syndrome occurs due to the deficiency of enzyme _____

N-Formimino glutamate (FIGLU) is an intermediate in the metabolism of _____.

What is the most common acquired cause for increased plasma tyrosine levels?_____

Phenylketonuria can be treated by large neutral amino acid supplementation, or use of commercially available BH4 also called as _____