Amino Acid Metabolism — Flashcards

People with a genetic deficiency of _____ present with hypermethioninemia

Urea has two nitrogen molecules, one from _____ and one from aspartate

The treatment for propionic acidemia is a low _____ diet that does not include valine, methionine, isoleucine, or threonine

Glutathione is a tripeptide composed of _____, CystEine and Glycine

In the muscle, amino acids transfer their NH3 group to _____, forming glutamate and -ketoacids

An odour of _____ is diagnostic of type 1 tyrosinemia and hypermethioninemia

_____ may be converted to methionine via the enzyme methionine synthase (with methyl-THF and vitamin B12 as cofactors)

After release from iodinated thyroglobulin, MIT and DIT are _____ by the enzyme thyroid deiodinase, reproducing I- and tyrosine

_____ is a dipeptide that is a marker of meat consumption

_____ is a dipeptide that can be found in excitable tissues like brain and muscle.