Amino Acid Metabolism — Flashcards

Phenylketones include _____, phenyllactate, and phenylpyruvate

In addition to enzyme deficiencies, homocystinuria may be caused by decreased affinity of _____ for pyridoxal phosphate (B6, active form)

What are the 9 (10*) essential amino acids? _____ValineThreonineTryptophan IsoleucineMethionineHistidine Arginine* during periods of growthLysineLeucine

Creatine is synthesized from _____, arginine, and methionine (GAM)

What enzyme deficiencies may cause homocystinuria? _____ and methionine synthase deficiencies

In the muscle, glutamate transfers its NH3 group to _____, forming alanine and -ketoglutarate

_____ is also called the 22nd amino acid and is encoded by UAG

In the kidney, glutamine may be broken down into _____ and glutamate via the enzyme glutaminase

Ornithine transcarbamylase (OTC) deficiency presents with _____ NH4+ and hyper-ammonemia

Pyruvate is converted to _____ via the enzyme alanine aminotransferase (ALT) (Cahill cycle)